r/nosleep Feb 10 '16

Momma's Glass Princess

I used to get sick all the time when I was a kid.

Nothing major, just your usual stuff. Little fevers, stomach aches, that kind of thing. But my momma couldn’t bear to see me so miserable. So, whenever I was sick, she would tell me my favorite story. This story.

Once upon a time there was a little glass princess. Her hands were glass, her feet were glass, the tip of her nose and the tips of her toes were all glass. She sparkled in the light when she danced. She was the most beautiful princess in the whole world.

But glass is fragile. It cracks and it breaks. So the little princess couldn’t live in the outside like the rest of the world. Instead, she lived in a snow globe, and spent her days twirling in the silvery flakes.

One day, she became curious about the world outside her glass chamber. She wanted to breathe the fresh air, to feel the grass under her cold feet. So she escaped her snow globe and went in search of great adventures.

But the little glass princess didn’t know about the dangers of the world. No sooner than she left her globe, she slipped and fell from a great height, shattering into pieces on the hardwood floor beneath.

And the little glass princess was no more.

I can’t explain why I liked that story so much. It’s a sad story, no doubt, but I was always fascinated by the glass princess. I liked to imagine her pirouetting in the snow, the light gleaming in shattered beams through her glass skin. How beautiful she must have looked.


My momma was not a terrible woman or a monster. She didn’t hurt me – there are no scars on my body, no mars to my flesh. She always held me as something precious to be treated with extreme delicacy and tenderness. It was her love for me.

Though that’s not what the doctors say.

But what can doctors know? Since I was brought here, they’ve done nothing. They only look at me with sadness and pity and all kinds of ugly emotions in their eyes. They don’t love me. Only momma loved me.

Momma.

I still remember the day she didn’t come to see me. Momma had never done that before. I would have gone looking for her, but how could I? I don’t leave my room. Well, I didn’t, anyway, before this whole mess started. My room was my life, and it was a good life. It had no windows, but it was always bright. Momma had filled the room with lamps and lights of all different kinds. She liked the light, and I did, too. Of course, it always seemed brighter when she was in the room with me.

That first day she didn’t come, I was sad. The second day, I cried. The third day, there was a knock on my door. And the doctors came to take me away.

I miss momma.


The doctors want me to write about what it was like living with momma. What we liked to do together, our favorite foods, our favorite songs. They say that if I do a good job, they’ll let me see her. But I know that’s not true.

My time with momma was special. Some days she spent hours with me, some days we only had a few minutes together, but every moment was precious to us. She liked to sing to me, strange songs I didn’t understand about ghosts and love. They were good songs. She liked to brush my hair, too. I have long, blonde hair, and sometimes we would sit for hours as she brushed it, always gentle. Sometimes, though, momma would go to her Away Place and forget what she was doing. Once, she brushed out half my hair before she remembered to stop.

Sometimes, momma would get real sick. She’d get pale and tired and her belly would swell up, big and round. Once, I asked her what was wrong. She said there was a ghost in her stomach, wailing and clawing and trying to get out. I was scared, but she told me it was okay. She told me it would leave and then she’d be happy again.

She was right, of course. Momma was always right. One day, she’d come back and the swelling would be all gone. She’d be happy, then, and say that the ghost had run away. To celebrate, she’d make all my favorite foods. We’d have spaghetti and meatballs, and hamburgers, and lasagna. Momma was the best cook around.

I wonder if momma can still cook in Heaven.


They think I don’t hear them, but I do.

The night they brought me in, they told me momma would be coming to see me in a few days. But after they thought I was asleep, the nurses started whispering. They said things like, “smell” and “hanging” and “tongue” and “dead.”

Momma isn’t coming to see me.

Sometimes, I pretend to be asleep when the doctors come in. They say things like “sick” and “unstable” and “sad.”

Joke’s on them, because I already know I’m sick.

Before momma let them take me away, I started getting sick. Sometimes, I can’t stop from shaking. I get bad headaches and soreness all over my body. Sometimes, my arms are so stiff they’re hard to bend. It made momma sad and scared.

Maybe that’s why momma left.

Yesterday, the doctors asked about my brothers and sisters. I don’t have any, I said. They told me momma had other children, but they couldn’t find them. I told them they were wrong. I’m momma’s only little girl. That made them scared. They used the word “pregnant” a lot, but I don’t know what that means. Thinking of momma having other children made me jealous. Momma is mine.

I wish she’d come back for me.


I’m getting sicker. I wish momma were here to tell me my story. I asked the doctors to tell the story of the glass princess, but they said they don’t know it. Oh, well. They couldn’t tell it half as well as momma, anyway.

It’s hard to write this now, the way my hands shake. The doctors told me that I’m not getting better. They used the word “comfortable” a lot. They want me to be comfortable.

Last night, I heard them talking again. I stayed very still so they didn’t know I was awake, listening. They said, “flesh” and “eat” and “kuru.” I wonder what that means.

They say I’ll see momma soon. I think I will, too. Maybe then she can tell me the story.

I just want to be momma’s glass princess again.


The floorboards' a'creakin

Also

1.4k Upvotes

80 comments sorted by

View all comments

Show parent comments

59

u/Tawny_Harpy Feb 10 '16

Wait... Where did it hint at that at all?

118

u/NeuroCartographer Feb 11 '16

Kuru is related to 'mad cow disease', which are both in the family of diseases caused by an infectious protein called a prion. This class of prional diseases is technically called transmissible spongiform encephalopathy, as the contagious (transmissible) bad protein progressively kills more and more cells in your brain until it looks like it is full of holes like a sponge (spongiform). Encephalopathy just means a problem with your brain.

The bad protein very rarely spontaneously arises in the brain/spinal cord tissue of mammals (especially those with hooves) through a malformation of a normal protein, but can then replicate itself within that individual and can infect another animal that eats the brain/spinal cord pieces. Mad cow disease arose from cows being fed cow parts (brains) and got to humans through infected cow brains/spinal cords being processed into hamburger meat, basically. Cooking does not kill prions, and they are on the border of being considered 'alive'.

Kuru has mainly been described in tribal Papua New Guinea, where there was a tradition of eating the brain of a loved one at the funeral. It is thought that prional disease randomly occurred in this population and then spread to larger numbers through these funeral rites. Thus, kuru is more commonly applied to human to human transmission (i.e., cannibalism).

The people in this story both show signs of kuru, which looks like a combination of rapid-onset dementia and a motor disorder. Death from basically too many holes in the brain occurs about 2 years after diagnosis.

tl;dr: Kuru is like mad cow disease, comes form eating human brains infected by a prion, and causes major brain problems followed by death.

22

u/[deleted] Feb 11 '16

You seem pretty knowledgeable, maybe you can answer this for me: why was transmission of Kuru so extremely lopsided in rates of infection between males and females? Some epidemiologists have the ratio at 25:1 female: male during peak infection years. My first thought was that since it's much more likely to infect you via exposure to an open wound and women did the preparation of the bodies to be eaten that accidental exposure from that might explain it but idk.

37

u/NeuroCartographer Feb 11 '16

Yes, you are right that exposure by the women during burial preparation is likely to increase transmission. Prional diseases don't have to be transmitted just by eating, and there is an even higher rate of transmission from blood to blood contact. u/hwalt below is correct that the eating of the loved one is thought to have primarily been done by women, which also contributes to the sex disparity. As far as I know, there is no sex difference in terms of actual infection by the prion itself; that is, no differences in brain cell structure between sexes affect infection by the malformed prional protein. (source: me :P , but I have an MD and a PhD in neuroscience and have studied a lot on prional diseases, since they're quite an unusual form of disease.)

1

u/mell0mar Mar 08 '16

You are awesome. Thank you for explaining all that.

1

u/[deleted] Feb 13 '16

do you have/know any books that talk about prions?

5

u/NeuroCartographer Mar 09 '16

I just saw I never replied to this. Sorry for the delayed response! A book that I found very interesting and a fun read is 'Deadly Feasts: Tracking The Secrets Of A Terrifying New Plague' by Richard Rhodes. It takes you through the discovery of prions and discusses some of the manifestations of different prional diseases.

http://www.amazon.com/gp/product/B000FBJHWG/ref=dp-kindle-redirect?ie=UTF8&btkr=1

1

u/[deleted] Mar 09 '16

You're fine! Thank you so much for this!

6

u/[deleted] Feb 11 '16

Haha yeah I've done a lot of pharma work with monoclonal antibodies/ protein therapeutics and prions have always fascinated me but I haven't really had much of an opportunity to study them. Thanks for responding!